Budd-Chiari Syndrome Revealing Behcet's Disease: A Case Report

The Budd-Chiari syndrome is a rare and serious complication of Behçet's disease, involving thrombosis of the hepatic veins and/or the intrahepatic or suprahepatic inferior vena cava. It primarily affects young men. We report the case of a 23-year-old patient admitted with Budd-Chiari syndrome accompanied by inferior vena cava thrombosis and deep vein thrombosis of the left lower limb. The patient was treated with curative anticoagulation and immunosuppressants, including methylprednisolone, cyclophosphamide, and azathioprine, resulting in significant clinical and biological improvement. Vascular Behçet's disease should be suspected in cases of recurrent venous and/or arterial thrombosis, as it is associated with high morbidity and mortality. Immunosuppressive treatment is essential for management.